Case Report
Volume: 4 | Issue: 10 | Published: Oct 28, 2020 | Pages: 357 - 359 | DOI: 10.24911/ejmcr/173-1597453071
Systemic aneurysms in a pediatric patient with congenital atrophoderma of Pasini and Pierini
Authors: Munaza Batool Rizvi
Article Info
Authors
Munaza Batool Rizvi
Childrens Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY, USA
Publication History
Received: August 15, 2020
Accepted: September 14, 2020
Published: October 28, 2020
Abstract
Background: Idiopathic Atrophoderma of Pasini and Pierini (IAPP) is a rare dermatological disease that has histopathological and epidemiological differences from morphea and linear atrophoderma of Moulin. Case Presentation: This is the first case, to the authors knowledge, describing multiple systemic arterial aneurysms in a patient with IAPP. Conclusion: More longitudinal studies are needed for patients with IAPP to determine if patients with congenital IAPP inherit a risk of developing arterial aneurysms later in life.
Keywords: Atrophoderma of Pasini and Pierini (IAPP), computed tomography angiography of the abdomen and pelvis (CTAP), magnetic resonance angiography (MRA), linear atrophoderma of Moulin (LAM), green
