Case Report
Volume: 4 | Issue: 11 | Published: Nov 06, 2020 | Pages: 384 - 386 | DOI: 10.24911/ejmcr/173-1589881846
Enterocutaneous fistula in a hemophilia B patient: case report
Authors: Sana Shahid , Hina Abdul Qayoom Khan , Summaya Saeed , Jan Muhammad Agha , Khursheed A. Samo , Mujeeb ur Rehman Abbasi , Amjad Siraj Memon
Article Info
Authors
Sana Shahid
Surgical Unit 3, Dow University of Health Sciences, Dr Ruth KM Pfau Civil Hospital Karachi, Karachi, Pakistan
Hina Abdul Qayoom Khan
Surgical Unit 3, Dow University of Health Sciences, Dr Ruth KM Pfau Civil Hospital Karachi, Karachi, Pakistan
Summaya Saeed
Surgical Unit 3, Dow University of Health Sciences, Dr Ruth KM Pfau Civil Hospital Karachi, Karachi, Pakistan
Jan Muhammad Agha
Surgical Unit 3, Dr Ruth KM Pfau Civil Hospital Karachi, Karachi, Pakistan
Khursheed A. Samo
Surgical Unit 3, Dow University of Health Sciences, Dr Ruth KM Pfau Civil Hospital Karachi, Karachi, Pakistan
Mujeeb ur Rehman Abbasi
Surgical Unit 3, Dow University of Health Sciences, Dr Ruth KM Pfau Civil Hospital Karachi, Karachi, Pakistan
Amjad Siraj Memon
Surgical Unit 3, Dow University of Health Sciences, Dr Ruth KM Pfau Civil Hospital Karachi, Karachi, Pakistan
Publication History
Received: May 19, 2020
Accepted: September 14, 2020
Published: November 06, 2020
Abstract
Background: Hemophilia B is a rare entity than other coagulation disorders. It is an X-linked disorder characterized by a deficiency of functionally active coagulation factor IX (FIX), resulting in spontaneous or trauma-induced bleeding primarily in joints, muscles, and soft tissues. Case Presentation: We report a case of a female who presented with a surgical problem. She had a history of massive transfusion many years back. She bled perioperatively and then we investigated her and luckily found the deficiency of FIX. She was managed and discharged home well. Conclusion: Surgeons rarely comes across this rare coagulation disorder, so this was an intriguing case in view of the unusual presentation, initial diagnostic dilemma, and challenges in management.
Keywords: Enterocutaneous fistula, hemophilia B, coagulation disorder, factor IX, case report, green
