Case Report

Volume: 7 | Issue: 7 | Published: Jan 11, 2024 | Pages: 137 - 139 | DOI: 10.24911/ejmcr/173-1684550572

Kasabach-Merritt Syndrome: A Case Report of a Giant Hepatic Hemangioma in an Adult.


Authors: Arturo G. Rosales , Javier A. Martinez orcid logo , Julio C. Ortiz-Cruz orcid logo , Anabel M. Garcia orcid logo , Dalia I. Murillo-Geraldo orcid logo , Carlos A. Garcia-Becerra


Authors

Arturo G. Rosales

Servicio de Terapia Intensiva, Hospital Puerta de Hierro Andares, Zapopan 45116, Mexico

Javier A. Martinez

Servicio de Terapia Intensiva, Hospital Puerta de Hierro Andares, Zapopan 45116, Mexico

orcid logo ORCID

Julio C. Ortiz-Cruz

Servicio de Terapia Intensiva, Hospital Puerta de Hierro Andares, Zapopan 45116, Mexico

orcid logo ORCID

Anabel M. Garcia

Servicio de Terapia Intensiva, Hospital Puerta de Hierro Andares, Zapopan 45116, Mexico

orcid logo ORCID

Dalia I. Murillo-Geraldo

Servicio de Terapia Intensiva, Hospital Puerta de Hierro Andares, Zapopan 45116, Mexico

orcid logo ORCID

Carlos A. Garcia-Becerra

Servicio de Terapia Intensiva, Hospital Puerta de Hierro Andares, Zapopan 45116, Mexico.

Publication History

Received: May 20, 2023

Revised: September 28, 2023

Accepted: September 28, 2023

Published: January 11, 2024


Abstract


Background: Hepatic Hemangioma (HH) is described as the most prevalent benign hepatic tumor, and it is usually discovered incidentally as a symptomless mass of less than 3 cm. Kasabach-Merritt Syndrome (KMS) is described as a rare but severe complication of some vascular tumors. This syndrome presents as severe thrombocytopenia accompanied with a consumptive coagulopathy. Case presentation: A 35-year-old female, with a history of a hepatic tumor that was incidentally diagnosed with an ultrasound, later develops abdominal distention, petechiae and prominent hematomas that appear with minimal trauma. At the initial approach are found hematological data of microangiopathic anemia, thrombocytopenia and consumptive coagulopathy accompanied with the histopathological and imaging diagnosis of a Giant HH. Conclusion: Although, it is a very rare complication, the severity of this Syndrome requires a prompt diagnosis and treatment.

Keywords: Kasabach-Merritt Syndrome, Hepatic Hemangioma, Giant Hepatic Hemangioma, Thrombocytopenia, Disseminated Intravascular Coagulation, Case Report, green