Case Report

Volume: 2 | Issue: 2 | Published: May 29, 2018 | Pages: 45 - 49 | DOI: 10.24911/ejmcr/2/13

Anesthetic considerations for a child with PHACE syndrome: a case report


Authors: Wadha Mubarak Alotaibi , Zainab Abdulaziz Alzayer


Article Info

Authors

Wadha Mubarak Alotaibi

Department of Anesthesia, College of Medicine, King Saud University, Riyadh, Saudi Arabia

Zainab Abdulaziz Alzayer

Imam Abdulrahman Bin Faisal University, King Fahad University Hospital. Dammam, Saudi Arabia

Publication History

Received: March 21, 2018

Revised: April 02, 2018

Accepted: April 04, 2018

Published: May 29, 2018


Abstract


Background: PHACE syndrome (Posterior fossa malformations-hemangiomas-arterial anomalies-cardiac defects-eye abnormalities-sternal cleft and supraumbilical raphe syndrome) is a rare and serious neurocutaneous disorder. Cerebrovascular and cardiac abnormalities are the most important anesthetic concerns for patients with PHACE syndrome in order to provide safe and sufficient perioperative anesthesia care. Case Presentation: The present case discussed anesthetic implications of an infant boy who had PHACE syndrome and presented for elective laparoscopic-assisted pull through procedure under general anesthesia. Conclusion: Certain perioperative anesthetic implications should be considered mainly for difficult airway management that related to airway hemangiomas, abnormal cerebrovascular structure mainly carotid arteries involvement that affect CBF and results in cerebral ischemia and the association of congenital cardiac disease.

Keywords: PHACE syndrome, anesthetic considerations, case report


Pubmed Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR. 2018; 29 (May 2018): 45-49. doi:10.24911/ejmcr/2/13

Web Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. https://ejmcr.com/articles/1568 [Access: December 25, 2024]. doi:10.24911/ejmcr/2/13

AMA (American Medical Association) Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR. 2018; 29 (May 2018): 45-49. doi:10.24911/ejmcr/2/13

Vancouver/ICMJE Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR. (2018), [cited December 25, 2024]; 29 (May 2018): 45-49. doi:10.24911/ejmcr/2/13

Harvard Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer (2018) Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR, 29 (May 2018): 45-49. doi:10.24911/ejmcr/2/13

Chicago Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. "Anesthetic considerations for a child with PHACE syndrome: a case report." 29 (2018), 45-49. doi:10.24911/ejmcr/2/13

MLA (The Modern Language Association) Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. "Anesthetic considerations for a child with PHACE syndrome: a case report." 29.May 2018 (2018), 45-49. Print. doi:10.24911/ejmcr/2/13

APA (American Psychological Association) Style

Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer (2018) Anesthetic considerations for a child with PHACE syndrome: a case report. , 29 (May 2018), 45-49. doi:10.24911/ejmcr/2/13