Case Report
Volume: 3 | Issue: 1 | Published: Jan 12, 2019 | Pages: 12 - 15 | DOI: 10.24911/ejmcr/173-1537696292
Spinal Epidural lipomatosis due to adrenal cortisol secreting adenoma in a 14 year old girl - a case report
Authors: Luna Bajracharya , Sharma Paudel
Article Info
Authors
Luna Bajracharya
Department of Pediatrics, Tribhuvan University Teaching Hospital, Kathmandu, Nepal
Sharma Paudel
Department of Radiology, Tribhuvan University Teaching Hospital, Kathmandu, Nepal
Publication History
Received: September 24, 2018
Revised: December 17, 2018
Accepted: December 18, 2018
Published: January 12, 2019
Abstract
Background: Spinal epidural lipomatosis (SEL) is an excessive fat deposition within the epidural space of spinal canal leading to compression of nervous structures and neurological manifestations. Exogenous glucocorticoid administration is the major cause of symptomatic SEL. The reported patient had SEL related to endogenous Cushing syndrome which is among few reported cases in the literature. Case presentation: A 14 year girl with features of Cushing syndrome had severe back pain and magnetic resonance imaging of spine showed SEL. Subsequently, computed tomography of abdomen showed right adrenal adenoma.The patient underwent adrenalectomy which improved her signs of hypercortisolism and SEL. Conclusion: In view of severe neurological deficits and therapeutic consequences, SEL should be considered in all patients with Cushing syndrome who present with symptoms of spinal cord compression. Correction of underlying endocrinopathy is imperative in management of SEL.
Keywords: Spinal epidural lipomatosis, Cushing syndrome, adrenal adenoma, case report, green
