Case Report
Volume: 4 | Issue: 8 | Published: Aug 11, 2020 | Pages: 270 - 274 | DOI: 10.24911/ejmcr/173-1591904275
The enigmatic challenge: secondary pulmonary arterial hypertension due to partial anomalous pulmonary venous return in a young woman
Authors: Ecaterina Sedaia , Valeriu Revenco , Andrei Esanu , Inesa Gutan , Viorica Ochisor , Alexandr Vascenco
Article Info
Authors
Ecaterina Sedaia
State University of Medicine and Pharmacy Nicolae Testemitanu, Department of Internal Medicine, Cardiology, Chisinau, Republic of Moldova
Valeriu Revenco
State University of Medicine and Pharmacy Nicolae Testemitanu, Department of Internal Medicine, Cardiology, Chisinau, Republic of Moldova
Andrei Esanu
State University of Medicine and Pharmacy Nicolae Testemitanu, Department of Internal Medicine, Cardiology, Chisinau, Republic of Moldova
Inesa Gutan
State University of Medicine and Pharmacy Nicolae Testemitanu, Department of Internal Medicine, Cardiology, Chisinau, Republic of Moldova
Viorica Ochisor
State University of Medicine and Pharmacy Nicolae Testemitanu, Department of Internal Medicine, Cardiology, Chisinau, Republic of Moldova
Alexandr Vascenco
Department of Arterial Hypertension, Institute of Cardiology, Chisinau, Republic of Moldova
Publication History
Received: June 11, 2020
Accepted: July 05, 2020
Published: August 11, 2020
Abstract
Background: Pulmonary arterial hypertension (PAH) involves many different clinical conditions and has an important impact on the right ventricular (RV) function and patients prognosis. Some of these conditions can be potentially curable, for example, congenital heart disease that could be surgically repaired. Case Presentation: We present a case of 41-year-old woman with a progressive shortness of breath, without evident explication. First, she was suspected to have chronic thromboembolic PAH, which was not confirmed by clinical and imaging data. Even arrhythmogenic RV cardiomyopathy was suspected according to the data obtained from the first cardiac magnetic resonance (CMR) imaging. However, due to a step-up in oxygen saturation during the right heart catheterization (RHC), the presence of rare congenital heart disease, such as partial anomalous of pulmonary venous return (PAPVR), was suspected and then confirmed by the repeated CMR. Conclusions: PAPVR is a rare congenital heart disease that could be suspected during the RHC and represents a potentially curable cause of PAH.
Keywords: Partial anomalous pulmonary venous return, pulmonary arterial hypertension, right ventricle, cardiac magnetic resonance, right heart catheterization, green
