ABSTRACT Background: Hydatid disease is a parasitic infection caused by the tapeworm Echinococcus granulosus.Intracranial hydatid cysts are rare and account for less than 3% of all cases of hydatid disease. Typically, these cysts are found in the intracerebral spaces. However, this study presents an extremely rare intradural hydatid cyst. Case presentation: This study presents the case of an 8-year-old boy presented with a 3-month history of headache and vomiting without any neurological deficit. Full radiological investigations were performed, and only a brain magnetic resonance imaging showed a large cerebral hydatid cyst located within the dura layers between the periosteal and the endosteal layers. Surgery was performed without cyst rupture, confirming the intracerebral intradural location. Conclusion: Early diagnosis and treatment for intracranial hydatid cysts are crucial to prevent complications such as neurological deficits, seizures, and even death. In this case, the intracerebral intradural location of the cyst is extremely rare.

Keywords: Intracranial, intradural, hydatid cysts, Echinococcus.