Background: Idiopathic Atrophoderma of Pasini and Pierini (IAPP) is a rare dermatological disease that has histopathological and epidemiological differences from morphea and linear atrophoderma of Moulin. Case Presentation: This is the first case, to the authors’ knowledge, describing multiple systemic arterial aneurysms in a patient with IAPP. Conclusion: More longitudinal studies are needed for patients with IAPP to determine if patients with congenital IAPP inherit a risk of developing arterial aneurysms later in life.

Keywords: Atrophoderma of Pasini and Pierini (IAPP), computed tomography angiography of the abdomen and pelvis (CTAP), magnetic resonance angiography (MRA), linear atrophoderma of Moulin (LAM)