Background: Heterotopic pancreas is the presence of pancreatic tissue outside its normal location, mostly in the gastrointestinal tract. It is rare and most patients are asymptomatic adults. The presence of heterotopic pancreas in the umbilicus and the pediatric age group is even more rare. Case Presentation: An 18-month-old boy presented with clear umbilical discharge since birth. On examination, there was a swollen and inflamed umbilicus. Exploration and excision of the umbilical lesion were done. Histopathological examination of the lesion reported as umbilical sinus with the presence of heterotopic pancreas. He was discharged well with no complications seen on the follow-up review. Conclusions: Heterotopic pancreas is rare. Awareness of this condition is important in order for the patient to be managed accordingly.

Keywords: Heterotopic pancreas, umbilicus, pediatric, umbilical sinus, case report