Anesthetic considerations for a child with PHACE syndrome: a case report
Authors: Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer
Background: PHACE syndrome (Posterior fossa malformations-hemangiomas-arterial anomalies-cardiac defects-eye abnormalities-sternal cleft and supraumbilical raphe syndrome) is a rare and serious neurocutaneous disorder. Cerebrovascular and cardiac abnormalities are the most important anesthetic concerns for patients with PHACE syndrome in order to provide safe and sufficient perioperative anesthesia care. Case Presentation: The present case discussed anesthetic implications of an infant boy who had PHACE syndrome and presented for elective laparoscopic-assisted pull through procedure under general anesthesia. Conclusion: Certain perioperative anesthetic implications should be considered mainly for difficult airway management that related to airway hemangiomas, abnormal cerebrovascular structure mainly carotid arteries involvement that affect CBF and results in cerebral ischemia and the association of congenital cardiac disease.
Keywords: PHACE syndrome, anesthetic considerations, case report
Authors
Correspondence to:
Wadha Mubarak Alotaibi, Associate professor, Department of Anesthesia, College of Medicine, King Saud University, Riyadh wadhm@yahoo.com
Publication history:
Received 21 Mar 2018
Revised 02 Apr 2018
Accepted 04 Apr 2018
Published online 29 May 2018
Published in print 29 May 2018
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR. 2018; 2(2): 45-49. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. https://www.ejmcr.com/?mno=294497 [Access: April 27, 2024]. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR. 2018; 2(2): 45-49. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR. (2018), [cited April 27, 2024]; 2(2): 45-49. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer (2018) Anesthetic considerations for a child with PHACE syndrome: a case report. EJMCR, 2 (2), 45-49. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. 2018. Anesthetic considerations for a child with PHACE syndrome: a case report. European Journal of Medical Case Reports, 2 (2), 45-49. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. "Anesthetic considerations for a child with PHACE syndrome: a case report." European Journal of Medical Case Reports 2 (2018), 45-49. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer. "Anesthetic considerations for a child with PHACE syndrome: a case report." European Journal of Medical Case Reports 2.2 (2018), 45-49. Print. doi:
10.24911/ejmcr/2/13
Wadha Mubarak Alotaibi, Zainab Abdulaziz Alzayer (2018) Anesthetic considerations for a child with PHACE syndrome: a case report. European Journal of Medical Case Reports, 2 (2), 45-49. doi:
10.24911/ejmcr/2/13